Neck neurofibromatosis: clinical and surgical features.

Type I Neurofibromatosis (NF1) is a dominant autosomal disease. Its prognosis is related to the development of tumors that may evolve to malignancy. It is characterized by multiple café-au-lait spots, skeletal defects, optical gliomas, Lisch nodules and neurofibromas. Plexiform neurofibromas (PN) are one of the many possible findings on patients affected by the disease. This paper aims at reporting on a case of a pediatric patient with cervical plexiform neurofibromas and the difficulties inherent to the treatment.